Case three: 2 year old boy showing two atonic-myoclonic-absence seizures at home
Video 1–54 seconds: Part A 31 seconds Clinical seizure onset at 19 seconds; Part B Clinical seizure onset at 40 seconds
Part A 2 year old boy is standing watching television intently with a spoon in his left hand. His eyes suddenly deviate upwards and he vocalizes as he crashes to the floor with atonia. He lands on his back with his legs in the air, his hands fling open and the spoon is dropped. His knees and arms flex and there are rhythmic beats of upper limb myoclonus. Consciousness returns rapidly with sobbing.
Part B The boy is seated watching television intently. He has a myoclonic jerk involving his face and upper limbs coupled with rapid elevation of his eyes. His head and body fall suddenly backwards with atonia and his upper limbs abduct with fingers extended. Oral automatisms are noted, followed by bilateral myoclonic jerks associated with ratcheting abduction of the upper limbs.
Case four: 5 year old boy showing atonic-myoclonic-absence seizures
The boy sits in bed playing a video game during video-EEG monitoring. There is clonic activity of his head associated with neck extension and atonia. His eyes deviate upwards with loss of facial expression. The upper limbs show myoclonic jerks with some flexion. There is rapid return of full awareness as he returns to playing the game.
Video 3 -10 seconds -Part B Clinical seizure onset at two seconds
The boy sits in bed watching the television. Myoclonus is seen in his left upper limb in concert with an atonic component, myoclonic movements of his neck and eye elevation.
7 year old boy self inducing seizures by bringing his face within centimeters of the television screen. An atonic headnod is accompanied by eye elevation and upper limb myoclonus. He then resumes stares intently at the television.
In the second part of the video, he again brings his face close to the television screen. He has recurrent atonic headnods at six seconds accompanied by upper limb myoclonic seizures often occurring in series with abduction.
Video 6 – 5 seconds - Part B – EEG monitoring - Clinical seizure onset at two seconds